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Overview
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The product of this gene is involved in peroxisome biosynthesis and integrity. It assembles membrane vesicles before the matrix proteins are translocated. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause Zellweger syndrome (ZWS).
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Overview
Immunohistochemistry of paraffin-embedded mouse kidney using PEX3 antibody (STJ29491) at dilution of 1:100 (40x lens).
Immunohistochemistry of paraffin-embedded human liver damage using PEX3 antibody (STJ29491) at dilution of 1:100 (40x lens).
Immunohistochemistry of paraffin-embedded rat kidney using PEX3 antibody (STJ29491) at dilution of 1:100 (40x lens).
Western blot analysis of extracts of various cell lines, using PEX3 antibody (STJ29491) at 1:1000 dilution._Secondary antibody: HRP Goat Anti-Rabbit IgG (H+L) at 1:10000 dilution._Lysates/proteins: 25ug per lane._Blocking buffer: 3% nonfat dry milk in TBST._Detection: ECL Enhanced Kit._Exposure time: 90s.
Anti-PEX3 antibody
Anti-PEX3 antibody
Catalog Number:
A001037471STJ
Mfr. No.:
STJ29491
Price:
$297
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