Name: MCCC1 Polyclonal Antibody (0.78 mg/mL) for WB, IHC, ELISA
Price: 253.00 USD

Overview
- Calculated MW: 80 kDa
  Observed MW: Refer to figures
  Gene Accession: BC004187
  
  Please contact us at for specific academic pricing.
  
  Background
  
  This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.
Properties
- Host
  
  rabbit
  
  Antibody Type
  
  polyclonal
  
  Isotype
  
  IgG
  
  Reactivity
  
  human; mouse
  
  Immunogen
  
  Fusion protein of human MCCC1
  
  Purification
  
  Antigen affinity purification
  
  Conjugate
  
  Unconjugated
  
  Formulation
  
  PBS with 0.05% NaN3 and 40% Glycerol, pH7.4
  
  Storage
  
  Store at -20°C. Avoid freeze-thaw cycles.
  
  Concentration
  
  0.78 mg/mL
  
  Antigen
  
  3-methylcrotonyl-CoA carboxylase 1, 3-methylcrotonyl-CoA carboxylase biotin-containing subunit, 3-methylcrotonyl-CoA carboxylase, alpha, 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha, DKFZp686B20267, FLJ25545, MCC-B, MCCA, MCCase subunit alpha, methylcrotonoyl-CoA carboxylase 1 (alpha), methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial, methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) (UniProt:Q96RQ3)
  
  * For reference only.