Name: Anti-MCCC1 antibody
Price: 297.00 USD

Overview
- This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.
  
  Please contact us at for specific academic pricing.
Properties
- Host
  
  rabbit
  
  Antibody Type
  
  polyclonal
  
  Isotype
  
  IgG
  
  Reactivity
  
  human; mouse
  
  Immunogen
  
  Recombinant fusion protein containing a sequence corresponding to amino acids 526-725 of human MCCC1 (NP_064551. 3).
  
  Purification
  
  Affinity purification
  
  Conjugate
  
  Unconjugated
  
  Formulation
  
  PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
  
  Storage
  
  Store at -20°C and avoid freeze-thaw cycles.
  
  Regulatory Status
  
  RUO
  
  Antigen
  
  Methylcrotonoyl-Coa Carboxylase Subunit Alpha-Mitochondrial; Mccase Subunit Alpha; 3-Methylcrotonyl-Coa Carboxylase 1; 3-Methylcrotonyl-Coa Carboxylase Biotin-Containing Subunit; 3-Methylcrotonyl-Coa-Carbon Dioxide Ligase Subunit Alpha (Gene ID:56922; UniProt:Q96RQ3)
  
  * For research use only